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Master Thesis

Efficience de deux tâches d’intelligibilité pour caractériser la dysarthrie dans l’ataxie de Friedreich

Abstract : The present study had three purposes: (1) to assess wether intelligibility could be a clinical severity marker for Friedreich’s Ataxia, by contrasting the MonPaGe intelligibility task (Fougeron, Delvaux, Ménard, & Laganaro, 2018) with the SARA severity ratings of this pathology (Schmitz-Hubsch et al., 2006); (2) to characterize the sensitivity of MonPaGe intelligibility task (Fougeron et al., 2018) in relation to the intelligibility phonetic test from the BECD (TPI-Batterie d’Évaluation Clinique de la Dysarthrie in Auzou & Rolland-Monnoury, 2006); (3) to uncover any correlation between bucco-linguo-facial motility impairments, as assessed by the MBLF-Motricité Bucco-Linguo-Faciale test (Gatignol & Lannadère, 2010), and intelligibility in Friedreich’s Ataxia. The studied population consisted of 35 patients (average age 36,6 years) genetically diagnosed with Friedreich's Ataxia. Performing 4 different kinds of tests, we studied 6 different types of the obtained data: intelligibility ratings and phonetic errors from each one of both intelligibility tests; ataxia severity ratings; specific bucco-linguo-facial motility impairments. The study results for this group of patients show that: (1) intelligibility can’t be a severity marker for Friedreich’s Ataxia as these two variables are not correlated; (2) we cannot assert that the MonPaGe intelligibility task has a better sensitivity than the TPI, however this study shows several qualities for the evaluation of intelligibility; (3) motility impairments are not directly correlated with phonetic errors, but we observed impairments in motility speed, as described in literature.
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Submitted on : Wednesday, June 24, 2020 - 10:22:10 AM
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  • HAL Id : dumas-02879670, version 1


Hélène Rance. Efficience de deux tâches d’intelligibilité pour caractériser la dysarthrie dans l’ataxie de Friedreich. Sciences cognitives. 2019. ⟨dumas-02879670⟩



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