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Master Thesis

Les manifestations orales et maxillo-faciales de la neurofibromatose de type 1 : revue systématique de la littérature et rapport d'un cas sévère

Abstract : Type 1 neurofibromatosis is an autosomal dominant phakomatosis whose prevalence is 1 in 4000. It is recognized that oral manifestations of the disorder are common. Clinical follow-up of a case severely affected by the disorder, including maxillofacial level allows us to take stock of the oral and maxillofacial manifestations of NF1. To this end, we carry out a systematic review of the French and Anglo-Saxon literature on oral and dento-maxillo-facial manifestations of the disorder. Then, we present the clinical case. The results of our review indicate that the soft tissues are more affected than hard tissue. The tongue is the organ most affected in the soft tissues while the mandible is the bone most affected among the hard tissue. Excluding the symmetrical appearance of the lesions of the serious case reported, the latter present oral abnormalities consistent with those found in the literature.
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Master Thesis
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https://dumas.ccsd.cnrs.fr/dumas-01128499
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Submitted on : Monday, March 9, 2015 - 5:56:15 PM
Last modification on : Wednesday, January 15, 2020 - 9:03:57 AM
Long-term archiving on: : Monday, April 17, 2017 - 5:49:59 AM

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Romain Nguyen. Les manifestations orales et maxillo-faciales de la neurofibromatose de type 1 : revue systématique de la littérature et rapport d'un cas sévère. Chirurgie. 2015. ⟨dumas-01128499⟩

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